Cardiovascular risk factors and increased carotid intima-media thickness in young patients with congenital adrenal hyperplasia due to 21-hydroxylase deficiency

Arch Endocrinol Metab. 2015 Dec;59(6):541-7. doi: 10.1590/2359-3997000000119.

Abstract

Objective: Increased arterial intima-media thickness has been observed in adults with congenital adrenal hyperplasia (CAH) due to 21-hydroxylase deficiency (21-OHD). CAH has also been associated with obesity, insulin resistance, and hypertension. The aim of the present study was to compare youths with CAH with healthy, normal-weight individuals, evaluating carotid intima-media thickness (CIMT) and indicative factors of cardiovascular risk to seek for abnormalities in the CAH group.

Subjects and methods: Clinical, biochemical, and ultrasonographic evaluations, according to published criteria, were performed in 113 subjects (5 to 20 years old): 40 patients with 21-OHD and 73 healthy individuals matched for gender, pubertal status, and age.

Results: Most CAH patients were female (80%), salt-losers (72.5%), and pubescent (80%); 10 (25%) patients were overweight. An increase in CIMT was observed both on the right (p = 0.0240) and left (p = 0.0003) sides in 38 CAH patients compared with the healthy individuals. The body mass index, BMI/age Z score, and systolic blood pressure (SBP) were higher in patients compared with controls (p < 0.000 and p = 0.0219, respectively).

Conclusions: Findings of increased CIMT, BMI, and SBP in young patients with 21-OHD indicate the need for early identification and intervention regarding cardiovascular risk. Validating these findings might result in improved therapeutic approaches for children with 21-OHD in the future.

Publication types

  • Comparative Study
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Adrenal Hyperplasia, Congenital / diagnostic imaging*
  • Adrenal Hyperplasia, Congenital / metabolism
  • Arterial Pressure / physiology*
  • Atherosclerosis / diagnostic imaging*
  • Body Mass Index*
  • Cardiovascular Diseases / diagnosis
  • Carotid Arteries / diagnostic imaging
  • Carotid Intima-Media Thickness*
  • Child
  • Child, Preschool
  • Female
  • Humans
  • Male
  • Overweight / diagnostic imaging
  • Risk Factors
  • Young Adult

Supplementary concepts

  • Congenital adrenal hyperplasia due to 21 hydroxylase deficiency