A case of acquired hemophilia A diagnosed after percutaneous endoscopic gastrostomy

Clin J Gastroenterol. 2015 Oct;8(5):290-3. doi: 10.1007/s12328-015-0601-z. Epub 2015 Sep 7.

Abstract

A 65-year-old male with no personal or familial history of bleeding disorders underwent percutaneous endoscopic gastrostomy (PEG) for neurogenic dysphagia due to subarachnoid hemorrhage. On postoperative day 6, continuous oozing of venous blood was observed at the stoma. Prothrombin time was within normal range, but activated partial thromboplastin time was prolonged. Cross-mixing test results indicated the existence of an inhibitor, and laboratory findings revealed decreased factor VIII activity and high levels of factor VIII inhibitor. The patient was diagnosed as having acquired hemophilia A, for which steroid monotherapy was effective. Acquired hemophilia A is a rare but potentially fatal disease. Clinicians should be aware of this condition in patients presenting with sudden hemorrhage after PEG or other endoscopic treatments, even in those with no apparent history of bleeding.

Keywords: Acquired hemophilia A; Endoscopic therapy; Factor VIII inhibitor; Immunosuppression; Percutaneous endoscopic gastrostomy.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Deglutition Disorders / surgery
  • Gastrostomy / adverse effects*
  • Hemophilia A / diagnosis*
  • Hemophilia A / drug therapy
  • Hemophilia A / etiology*
  • Humans
  • Immunosuppressive Agents / therapeutic use
  • Male
  • Postoperative Hemorrhage / complications
  • Prednisolone / therapeutic use

Substances

  • Immunosuppressive Agents
  • Prednisolone

Supplementary concepts

  • Factor 8 deficiency, acquired