Myelolipoma is a rare, benign, endocrinologically nonfunctioning adrenal tumor composed of fatty tissue with foci of hematopoietic cells. Clinical diagnosis and surgical removal are extremely rare. We report a case of large myelolipoma (10 x 6 x 6 cm) that was removed surgically in a 54-year-old man in whom the mass was studied preoperatively by sonogram, CT and angiography.