The utility of IgM, CD21, HGAL and LMO2 in the diagnosis of pediatric follicular lymphoma

Hum Pathol. 2015 Apr;46(4):629-33. doi: 10.1016/j.humpath.2014.12.016. Epub 2015 Jan 29.

Abstract

Pediatric follicular lymphoma (pFL) is a rare neoplasm with features differing from follicular lymphoma arising in adults. Here, we describe a rare case of pFL that showed morphologic features partially overlapping with progressive transformation of germinal centers and reactive follicular hyperplasia. As typical of pFL, neoplastic B cells within follicles did not express B-cell leukemia/lymphoma 2 (BCL2). However, this case showed additional distinctive abnormal findings, which contributed to the diagnosis: (1) diffuse and uniform staining of immunoglobulin M (IgM) on cells within and outside of follicles, (2) abnormally dim expression of CD21 on follicular dendritic cells, and (3) expression of human germinal center-associated lymphoma (HGAL) and LIM domain only 2 (LMO2) on B cells in interfollicular and follicular areas. This case demonstrates the utility of these abnormal features, which can be seen in adult- or usual-type follicular lymphoma, in the diagnosis of pFL. Further studies are necessary to evaluate the significance of these findings in other cases of pFL.

Keywords: Adult follicular lymphoma; HGAL; IgM; LMO2; Pediatric follicular lymphoma.

Publication types

  • Case Reports

MeSH terms

  • Adaptor Proteins, Signal Transducing / metabolism*
  • B-Lymphocytes / pathology
  • Biomarkers, Tumor / metabolism*
  • Child
  • Germinal Center / pathology
  • Humans
  • Immunoglobulin M / immunology
  • Immunoglobulin M / metabolism*
  • Intracellular Signaling Peptides and Proteins
  • LIM Domain Proteins / metabolism*
  • Lymphoma, Follicular / diagnosis*
  • Lymphoma, Follicular / metabolism*
  • Male
  • Microfilament Proteins
  • Neoplasm Proteins / metabolism*
  • Proto-Oncogene Proteins / metabolism*
  • Receptors, Complement 3d / metabolism*

Substances

  • Adaptor Proteins, Signal Transducing
  • Biomarkers, Tumor
  • GCSAM protein, human
  • Immunoglobulin M
  • Intracellular Signaling Peptides and Proteins
  • LIM Domain Proteins
  • LMO2 protein, human
  • Microfilament Proteins
  • Neoplasm Proteins
  • Proto-Oncogene Proteins
  • Receptors, Complement 3d