Effects of deep brain stimulation in relatively young-onset multiple system atrophy Parkinsonism

J Neurol Sci. 2014 Jul 15;342(1-2):42-4. doi: 10.1016/j.jns.2014.04.022. Epub 2014 Apr 29.

Abstract

Objective: The aim of this study was to analyze outcomes after 1 year of bilateral STN deep brain stimulation (DBS) in relatively young-onset patients with multiple system atrophy-Parkinsonism (MSA-P).

Background: The efficacy of DBS has been demonstrated in idiopathic Parkinson's disease. However, the experience with DBS in relatively young-onset MSA-P is limited and controversial.

Methods: Information about the demographic and clinical data from five MSA patients treated with STN DBS was entered into a database and analyzed.

Results: Five patients with relatively young-onset MSA (mean age at onset 42.2±2.2 years, 3 women, 2 men) have been treated with bilateral STN stimulators, the mean duration between DBS surgery and disease onset was 7.0±3.5 years. All of the patients had dyskinesia and postural instability, and subjective benefit from levodopa. During the 6 months after surgery, the clinical status of three patients improved with a decrease of dyskinesia. However, by 1 year, the symptoms reappeared and progressed in all patients. Overall, the mean "off" medication UPDRS-III score worsened 23.5±15.3 1 year after surgery and the levodopa dosage was not reduced.

Conclusions: This data does not support the use of STN DBS for relatively young-onset MSA-P.

Keywords: Deep brain stimulation; Multiple system atrophy; Parkinson's disease; Subthalamic nucleus; Young-onset.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Age of Onset
  • Deep Brain Stimulation*
  • Female
  • Humans
  • Male
  • Multiple System Atrophy / complications
  • Multiple System Atrophy / epidemiology*
  • Multiple System Atrophy / therapy*
  • Parkinsonian Disorders / complications
  • Parkinsonian Disorders / epidemiology*
  • Parkinsonian Disorders / therapy*
  • Retrospective Studies
  • Subthalamic Nucleus / physiology*
  • Treatment Outcome
  • Young Adult