A cerebellopontine angle lipoma accompanied by a bony protrusion from the left petrous pyramid was discovered in a 35-year-old female with a 10-year history of vertigo and a 3-year history of left tinnitus. Following subtotal removal of the tumor, the frequency of vertigo increased and she was deaf in the left ear. The symptoms, radiological and pathological features, and surgical management of this rare tumor are discussed.