PARK2/Parkin-mediated mitochondrial clearance contributes to proteasome activation during slow-twitch muscle atrophy via NFE2L1 nuclear translocation

Autophagy. 2014 Apr;10(4):631-41. doi: 10.4161/auto.27785. Epub 2014 Jan 21.

Abstract

Skeletal muscle atrophy is thought to result from hyperactivation of intracellular protein degradation pathways, including autophagy and the ubiquitin-proteasome system. However, the precise contributions of these pathways to muscle atrophy are unclear. Here, we show that an autophagy deficiency in denervated slow-twitch soleus muscles delayed skeletal muscle atrophy, reduced mitochondrial activity, and induced oxidative stress and accumulation of PARK2/Parkin, which participates in mitochondrial quality control (PARK2-mediated mitophagy), in mitochondria. Soleus muscles from denervated Park2 knockout mice also showed resistance to denervation, reduced mitochondrial activities, and increased oxidative stress. In both autophagy-deficient and Park2-deficient soleus muscles, denervation caused the accumulation of polyubiquitinated proteins. Denervation induced proteasomal activation via NFE2L1 nuclear translocation in control mice, whereas it had little effect in autophagy-deficient and Park2-deficient mice. These results suggest that PARK2-mediated mitophagy plays an essential role in the activation of proteasomes during denervation atrophy in slow-twitch muscles.

Keywords: NFE2L1; PARK2-mediated mitophagy; autophagy; knockout mouse; mitochondria; proteasome; skeletal muscle atrophy; slow-twitch muscle.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Active Transport, Cell Nucleus
  • Animals
  • Autophagy / genetics*
  • Autophagy / physiology
  • Enzyme Activation
  • Mice
  • Mice, Knockout
  • Mitochondria / metabolism*
  • Mitophagy / physiology*
  • Muscular Atrophy / metabolism*
  • NF-E2-Related Factor 1 / metabolism*
  • Proteasome Endopeptidase Complex / metabolism*
  • Ubiquitin / metabolism
  • Ubiquitin-Protein Ligases / metabolism*

Substances

  • NF-E2-Related Factor 1
  • Nfe2L1 protein, mouse
  • Ubiquitin
  • Ubiquitin-Protein Ligases
  • parkin protein
  • Proteasome Endopeptidase Complex