Chromosome evolution and high-resolution analysis of leucocytes, bone marrow, and tumor cells of retinoblastoma patients

Am J Med Genet. 1990 Aug;36(4):456-62. doi: 10.1002/ajmg.1320360417.

Abstract

High-resolution cytogenetics were applied to leucocytes, bone marrow, and tumors of 8 retinoblastoma (Rb) patients in search of microdeletions or subtle rearrangements and in order to determine clonal evolution. Four of 9 tumors (Rb1, Rb6.1, Rb6.2, and Rb8) showed a deletion in the characteristic region on 13q while 2 others (Rb3 and Rb4) were hemizygous for chromosome 13 in approximately one-third of the cells. Our study presents a particularly high incidence of chromosome 13 anomalies as compared to the previously published data. Furthermore, comparison of karyotypes of 3 significant cases (Rb1, Rb6, and Rb8) allows the reconstruction of the necessary steps in the evolution of retinoblastoma. It also shows the need for a double mutation in tumor development, both in hereditary and non-hereditary cases. High-resolution chromosome analysis of retinoblastoma patients provides a rare opportunity to study the succession of events necessary for tumor development.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Bone Marrow / ultrastructure*
  • Child, Preschool
  • Chromosome Banding
  • Chromosome Deletion*
  • Chromosomes, Human, Pair 13
  • Eye Neoplasms / genetics*
  • Eye Neoplasms / ultrastructure
  • Gene Rearrangement*
  • Humans
  • Infant
  • Karyotyping
  • Leukocytes / ultrastructure*
  • Retinoblastoma / genetics*
  • Retinoblastoma / ultrastructure