Surgery for congenital aortic stenosis in children with left ventricular noncompaction

J Card Surg. 2013 Jul;28(4):465-6. doi: 10.1111/jocs.12132. Epub 2013 Jun 14.

Abstract

Left ventricular noncompaction (LVNC) is an uncommon genetic disorder of endocardial morphogenesis, which carries a high mortality from heart failure or sudden cardiac death. This condition is often first diagnosed in adults, but it has also been described in children with other cardiac anomalies. We discuss the management of a 10-year-old female with congenital aortic stenosis associated with LVNC.

Publication types

  • Case Reports

MeSH terms

  • Animals
  • Aortic Stenosis, Subvalvular / congenital*
  • Aortic Stenosis, Subvalvular / diagnostic imaging
  • Aortic Stenosis, Subvalvular / surgery*
  • Aortic Valve / surgery*
  • Cardiac Valve Annuloplasty / methods*
  • Cattle
  • Child
  • Echocardiography, Transesophageal
  • Female
  • Heart Ventricles / abnormalities*
  • Heart Ventricles / diagnostic imaging
  • Humans
  • Intraoperative Period
  • Pericardium / transplantation
  • Treatment Outcome
  • Vascular Surgical Procedures / methods
  • Ventricular Dysfunction, Left / congenital*
  • Ventricular Dysfunction, Left / diagnostic imaging