The tracheobronchial glands are considered to be counterparts of the minor salivary glands in the respiratory tract and can develop similar tumors (tumors of salivary gland type). Within this group of neoplasia epithelial-myoepithelial carcinoma of the respiratory tract is very rare and the diagnosis is often difficult. The first case of this tumor entity in the trachea is reported and a review of the literature on these tumors is presented. The exact histological classification as well as the localization and the endoscopic findings of these lesions are crucial for therapeutic decision-making.