Gaucher disease: hematologic and oncologic implications

Clin Adv Hematol Oncol. 2011 Oct;9(10):771-2.
No abstract available

MeSH terms

  • 1-Deoxynojirimycin / administration & dosage
  • 1-Deoxynojirimycin / analogs & derivatives
  • 1-Deoxynojirimycin / therapeutic use
  • Carcinoma, Hepatocellular / complications
  • Carcinoma, Hepatocellular / drug therapy*
  • Carcinoma, Hepatocellular / pathology
  • Enzyme Inhibitors / administration & dosage
  • Enzyme Inhibitors / therapeutic use
  • Enzyme Replacement Therapy
  • Gaucher Disease / complications
  • Gaucher Disease / drug therapy*
  • Gaucher Disease / pathology
  • Glucosylceramidase / administration & dosage
  • Glucosylceramidase / therapeutic use
  • Glucosyltransferases / antagonists & inhibitors
  • Glucosyltransferases / metabolism
  • Humans
  • Liver / enzymology
  • Liver / pathology
  • Multiple Myeloma / complications
  • Multiple Myeloma / drug therapy*
  • Multiple Myeloma / pathology
  • Risk Factors
  • Spleen / enzymology
  • Spleen / pathology
  • Spleen / surgery
  • Splenectomy

Substances

  • Enzyme Inhibitors
  • 1-Deoxynojirimycin
  • miglustat
  • Glucosyltransferases
  • ceramide glucosyltransferase
  • Glucosylceramidase
  • imiglucerase