Abstract
Mixed gonadal dysgenesis is a disorder of sexual differentiation, characterized by mosaicism, ambiguous external genitalia, and both Wolffian and Müllerian internal genitalia. These patients are at a known increased risk of germ cell cancer, specifically gonadoblastoma; however, in this report we describe a case of adenocarcinoma of a remnant Müllerian structure.
Copyright © 2012 Elsevier Inc. All rights reserved.
MeSH terms
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Adenocarcinoma / epidemiology*
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Adenocarcinoma / pathology
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Adenosarcoma / epidemiology*
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Adenosarcoma / pathology
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Adult
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Comorbidity
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Female
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Gonadal Dysgenesis, Mixed / diagnosis
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Gonadal Dysgenesis, Mixed / epidemiology*
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Gonadal Dysgenesis, Mixed / pathology
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Humans
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Magnetic Resonance Imaging
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Male
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Uterine Neoplasms / epidemiology*
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Uterine Neoplasms / pathology
Supplementary concepts
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Adenosarcoma of the uterus