[Systemic amyloidoses]

Internist (Berl). 2012 Jan;53(1):51-64. doi: 10.1007/s00108-011-2952-y.
[Article in German]

Abstract

Amyloidoses are rare protein folding disorders, in which proteins are deposited as insoluble fibrillar aggregates due to a conformational change. This can occur in a local or systemic form. Systemic amyloidoses are life-threatening complications of monoclonal gammopathy, chronic inflammatory diseases or within hereditary diseases. The causative treatment of amyloidosis is the reduction of the amyloid precursor protein by chemotherapy, anti-inflammatory treatment, or liver transplantation. Early diagnosis of the disease is essential in order to effectively treat patients and avoid further deterioration of organ functions.

Publication types

  • English Abstract

MeSH terms

  • Amyloidosis / diagnosis*
  • Amyloidosis / therapy*
  • Humans
  • Inflammation / complications
  • Inflammation / diagnosis*
  • Inflammation / therapy*
  • Paraproteinemias / complications
  • Paraproteinemias / diagnosis*
  • Paraproteinemias / therapy*