A 64-year-old man was referred to our hospital for the treatment of left renal cell carcinoma associated with a tumor located on the back of the inferior vena cava. At first the tumor located on the back of the inferior vena cava was suspected to be lymphnode metastasis of renal cell carcinoma. A more detailed examination at our hospital revealed elevation of vanillylmandelic acid in urine and (131)Imetaiodobenzylguanidine uptake in the tumor. We diagnosed the tumor as paraganglioma and operated both tumors at the same time. Histological examination revealed chromophobe renal cell carcinoma and paraganglioma. His important to discriminate paraganglioma in the renal cell carcinoma that has an atypical swelling of lymphnode.