Complement inhibition alleviates paraquat-induced acute lung injury

Am J Respir Cell Mol Biol. 2011 Oct;45(4):834-42. doi: 10.1165/rcmb.2010-0444OC. Epub 2011 Mar 18.

Abstract

The widely used herbicide, paraquat (PQ), is highly toxic and claims thousands of lives from both accidental and voluntary ingestion. The pathological mechanisms of PQ poisoning-induced acute lung injury (ALI) are not well understood, and the role of complement in PQ-induced ALI has not been elucidated. We developed and characterized a mouse model of PQ-induced ALI and studied the role of complement in the pathogenesis of PQ poisoning. Intraperitoneal administration of PQ caused dose- and time-dependent lung damage and mortality, with associated inflammatory response. Within 24 hours of PQ-induced ALI, there was significantly increased expression of the complement proteins, C1q and C3, in the lung. Expression of the anaphylatoxin receptors, C3aR and C5aR, was also increased. Compared with wild-type mice, C3-deficient mice survived significantly longer and displayed significantly reduced lung inflammation and pathology after PQ treatment. Similar reductions in PQ-induced inflammation, pathology, and mortality were recorded in mice treated with the C3 inhibitors, CR2-Crry, and alternative pathway specific CR2-fH. A similar therapeutic effect was also observed by treatment with either C3a receptor antagonist or a blocking C5a receptor monoclonal antibody. Together, these studies indicate that PQ-induced ALI is mediated through receptor signaling by the C3a and C5a complement activation products that are generated via the alternative complement pathway, and that complement inhibition may be an effective clinical intervention for postexposure treatment of PQ-induced ALI.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Acute Lung Injury / chemically induced
  • Acute Lung Injury / genetics
  • Acute Lung Injury / immunology
  • Acute Lung Injury / pathology
  • Acute Lung Injury / prevention & control*
  • Animals
  • Anti-Inflammatory Agents / pharmacology*
  • Antibodies, Monoclonal / pharmacology
  • Complement Activation / drug effects*
  • Complement Activation / genetics
  • Complement C1q / metabolism
  • Complement C3 / antagonists & inhibitors
  • Complement C3 / genetics
  • Complement C3 / metabolism
  • Disease Models, Animal
  • Lung / drug effects*
  • Lung / immunology
  • Lung / pathology
  • Mice
  • Mice, Inbred C57BL
  • Mice, Knockout
  • Paraquat*
  • Receptor, Anaphylatoxin C5a / antagonists & inhibitors
  • Receptor, Anaphylatoxin C5a / metabolism
  • Receptors, Complement / antagonists & inhibitors
  • Receptors, Complement / metabolism
  • Recombinant Fusion Proteins / pharmacology
  • Signal Transduction / drug effects
  • Time Factors

Substances

  • Anti-Inflammatory Agents
  • Antibodies, Monoclonal
  • CR2-Crry fusion protein, mouse
  • Complement C3
  • Receptor, Anaphylatoxin C5a
  • Receptors, Complement
  • Recombinant Fusion Proteins
  • complement C3a receptor
  • Complement C1q
  • Paraquat