Hepatoblastoma represents the child's most frequent malignant hepatic tumor. We present the case of a one-year old prematurely born patient with an abdominal mass. Ultrasound and CT scan demonstrated a solid hepatic tumor. Serum alpha fetoprotein level was increased. He presented thrombocytosis and a left lobe hepatectomy was performed. Pathological examination revealed complete excision of a mixed hepatoblastoma. Hepatic tumor at a child under 3 years old correlated with elevated serum alpha fetoprotein and thrombocytosis are almost patognomonic for hepatoblastoma. Complete surgery is the mainstay of therapy in hepatoblastoma.