The IgH 3' regulatory region and its implication in lymphomagenesis

Eur J Immunol. 2010 Dec;40(12):3306-11. doi: 10.1002/eji.201040778.

Abstract

The 3' regulatory region (3'RR) located downstream of the IgH gene is the master element that controls class switch recombination and sustains high-level transcription at the plasma-cell stage. This latter role suggests that the 3'RR may be involved in oncogene deregulation during the frequent IgH translocation events associated with B-cell malignancies. A convincing demonstration of the essential contribution of 3'RR in lymphomagenesis has been provided by transgenic animal models. The mouse 3'RR shares a strong structural homology with the regulatory regions located downstream of each human Cα gene. Mouse models exploring the role of the 3'RR in B-cell physiology and in malignancies should provide useful indications about the pathophysiology of human cell lymphocyte proliferation.

Publication types

  • Research Support, Non-U.S. Gov't
  • Review

MeSH terms

  • 3' Untranslated Regions / genetics*
  • 3' Untranslated Regions / immunology
  • Animals
  • B-Lymphocytes / immunology*
  • Cell Transformation, Neoplastic / genetics
  • Cell Transformation, Neoplastic / immunology
  • Disease Models, Animal
  • Humans
  • Immunoglobulin Heavy Chains / genetics*
  • Lymphoma / genetics*
  • Lymphoma / pathology
  • Mice
  • Mice, Transgenic
  • Regulatory Sequences, Nucleic Acid / genetics*
  • Regulatory Sequences, Nucleic Acid / immunology

Substances

  • 3' Untranslated Regions
  • Immunoglobulin Heavy Chains