BCL6 is critical for the development of a diverse primary B cell repertoire

J Exp Med. 2010 Jun 7;207(6):1209-21. doi: 10.1084/jem.20091299. Epub 2010 May 24.

Abstract

BCL6 protects germinal center (GC) B cells against DNA damage-induced apoptosis during somatic hypermutation and class-switch recombination. Although expression of BCL6 was not found in early IL-7-dependent B cell precursors, we report that IL-7Ralpha-Stat5 signaling negatively regulates BCL6. Upon productive VH-DJH gene rearrangement and expression of a mu heavy chain, however, activation of pre-B cell receptor signaling strongly induces BCL6 expression, whereas IL-7Ralpha-Stat5 signaling is attenuated. At the transition from IL-7-dependent to -independent stages of B cell development, BCL6 is activated, reaches expression levels resembling those in GC B cells, and protects pre-B cells from DNA damage-induced apoptosis during immunoglobulin (Ig) light chain gene recombination. In the absence of BCL6, DNA breaks during Ig light chain gene rearrangement lead to excessive up-regulation of Arf and p53. As a consequence, the pool of new bone marrow immature B cells is markedly reduced in size and clonal diversity. We conclude that negative regulation of Arf by BCL6 is required for pre-B cell self-renewal and the formation of a diverse polyclonal B cell repertoire.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • ADP-Ribosylation Factors / metabolism
  • Animals
  • Apoptosis
  • B-Lymphocytes / cytology*
  • B-Lymphocytes / immunology*
  • Base Sequence
  • Cell Proliferation
  • Cell Survival
  • Cells, Cultured
  • Cytoprotection
  • DNA Damage / genetics
  • DNA-Binding Proteins / immunology*
  • Down-Regulation / genetics
  • Gene Rearrangement, B-Lymphocyte, Light Chain / genetics
  • Humans
  • Interleukin-7 / metabolism
  • Lymphopoiesis
  • Mice
  • Molecular Sequence Data
  • Pre-B Cell Receptors / metabolism
  • Precursor Cells, B-Lymphoid / cytology
  • Precursor Cells, B-Lymphoid / metabolism
  • Proto-Oncogene Proteins c-bcl-6
  • Proto-Oncogene Proteins c-myc / metabolism
  • Recombination, Genetic / genetics
  • Signal Transduction
  • Transcription, Genetic
  • Up-Regulation / genetics

Substances

  • Bcl6 protein, mouse
  • DNA-Binding Proteins
  • Interleukin-7
  • Pre-B Cell Receptors
  • Proto-Oncogene Proteins c-bcl-6
  • Proto-Oncogene Proteins c-myc
  • ADP-Ribosylation Factors