A unique interaction between alphaIIb and beta3 in the head region is essential for outside-in signaling-related functions of alphaIIbbeta3 integrin

Blood. 2010 Jun 3;115(22):4542-50. doi: 10.1182/blood-2009-10-251066. Epub 2010 Mar 22.

Abstract

The main interface of the 2 subunits of platelet integrin alphaIIbbeta3 comprises the beta-propeller domain of alphaIIb and the betaA domain of beta3. In the center of the beta-propeller, several aromatic residues interact by cation-pi and hydrophobic bonds with Arg261 of betaA. In this study, we substituted alphaIIb-Trp110 or beta3-Arg261 by residues abundant in other alpha or beta subunits at corresponding locations and expressed them in baby hamster kidney cells along with normal beta3 or alphaIIb, respectively. These mutant cells displayed normal surface expression and fibrinogen binding but grossly impaired outside-in signaling-related functions: adhesion to immobilized fibrinogen, cell spreading, focal adhesion kinase phosphorylation, clot retraction, and reduced alphaIIbbeta3 stability in EDTA (ethylenediaminetetraacetic acid). Expression of mutants with substitutions of Arg261 in beta3 by alanine or lysine with normal alphav yielded normal surface expression of alphavbeta3 and soluble fibrinogen binding as well as normal outside-in signaling-related functions, contrasting findings for alphaIIbbeta3. Structural analysis of alphaIIbbeta3 and alphavbeta3 revealed that alphavbeta3 has several strong interactions between alphav and beta3 subunits that are missing in alphaIIbbeta3. Together, these findings indicate that the interaction between Trp110 of alphaIIb and Arg261 of beta3 is critical for alphaIIbbeta3 integrity and outside-in signaling-related functions.

MeSH terms

  • Amino Acid Sequence
  • Amino Acid Substitution
  • Animals
  • Base Sequence
  • Binding Sites / genetics
  • Clot Retraction
  • Cricetinae
  • DNA Primers / genetics
  • Fibrinogen / metabolism
  • Humans
  • Hydrophobic and Hydrophilic Interactions
  • In Vitro Techniques
  • Integrin alphaV / chemistry
  • Integrin alphaV / genetics
  • Integrin alphaV / metabolism
  • Integrin beta3 / chemistry*
  • Integrin beta3 / genetics
  • Integrin beta3 / metabolism*
  • Models, Molecular
  • Molecular Sequence Data
  • Mutagenesis, Site-Directed
  • Platelet Membrane Glycoprotein IIb / chemistry*
  • Platelet Membrane Glycoprotein IIb / genetics
  • Platelet Membrane Glycoprotein IIb / metabolism*
  • Protein Binding
  • Protein Interaction Domains and Motifs
  • Protein Stability
  • Recombinant Proteins / chemistry
  • Recombinant Proteins / genetics
  • Recombinant Proteins / metabolism
  • Sequence Homology, Amino Acid
  • Signal Transduction
  • Transfection
  • von Willebrand Factor / metabolism

Substances

  • DNA Primers
  • Integrin alphaV
  • Integrin beta3
  • Platelet Membrane Glycoprotein IIb
  • Recombinant Proteins
  • von Willebrand Factor
  • Fibrinogen