Aortic valve replacement in a patient with Osler-Rendu-Weber disease

Ann Thorac Surg. 2009 Jul;88(1):e3-4. doi: 10.1016/j.athoracsur.2009.02.014.

Abstract

Osler-Rendu-Weber (hereditary hemorrhagic telangiectasia) disease is an uncommon disease characterized by the presence of abnormal telangiectasias and arteriovenous malformations that cause recurrent episodes of bleeding. We present a patient with Osler-Rendu-Weber disease, with a history of multiple major bleeding events and severe aortic valve stenosis, who underwent aortic valve replacement. Unexpectedly, the postoperative course was uneventful, and there was no untoward bleeding in the early or in the late postoperative follow-up.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Aortic Valve Stenosis / complications
  • Aortic Valve Stenosis / diagnostic imaging
  • Aortic Valve Stenosis / surgery*
  • Echocardiography, Doppler
  • Follow-Up Studies
  • Heart Valve Prosthesis Implantation / methods*
  • Heart Valve Prosthesis*
  • Humans
  • Male
  • Middle Aged
  • Rare Diseases
  • Risk Assessment
  • Severity of Illness Index
  • Telangiectasia, Hereditary Hemorrhagic / complications
  • Telangiectasia, Hereditary Hemorrhagic / diagnosis*
  • Treatment Outcome