Lymphoproliferative disorders after immunosuppressive therapy for aplastic anemia: a case report and literature review

Acta Haematol. 2009;121(1):21-6. doi: 10.1159/000209225. Epub 2009 Mar 18.

Abstract

A 61-year-old Japanese man was referred to our hospital in 2002 due to severe pancytopenia. Bone marrow and peripheral blood findings indicated he had severe aplastic anemia (AA). A whole-body CT scan and Ga scintigraphy revealed no abnormal findings. Antithymocyte globulin and cyclosporine A (CyA) were administered and he got transfusion independently. In September 2004, he complained of abdominal fullness and a skin eruption in the lower abdomen. An abdominal CT revealed a spleen mass and lymphoadenopathy of the pancreas head. Splenectomy was done, and he was diagnosed with a diffuse large B cell lymphoma (DLBCL) of the spleen and skin. His karyotype was associated with t(14; 18). CyA was stopped, all lesions disappeared, and then his AA relapsed. In January 2007, antithymocyte globulin/CyA was readministered. In May 2007, he complained of acute swelling in his right thigh. A biopsy from the tumor revealed DLBCL. CyA was stopped again, yet the lymphoma did not regress. He was given R-CHOP (rituximab, cyclophosphamide, doxorubicin hydrochloride, vincristine, prednisolone), followed by 5 cycles of R-VP (rituximab, vincristine, prednisolone) and radiation therapy, resulting in a partial remission. We report DLBCL after immunosuppressive therapy for AA. Although this is a rare complication, it should be considered before beginning immunosuppressive therapy.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Anemia, Aplastic / complications*
  • Anemia, Aplastic / pathology
  • Anemia, Aplastic / therapy
  • Antibodies, Monoclonal / administration & dosage
  • Antibodies, Monoclonal, Murine-Derived
  • Antilymphocyte Serum / administration & dosage
  • Antilymphocyte Serum / adverse effects
  • Antineoplastic Combined Chemotherapy Protocols / administration & dosage
  • Asian People
  • Cyclophosphamide / administration & dosage
  • Cyclosporine / administration & dosage
  • Cyclosporine / adverse effects
  • Doxorubicin / administration & dosage
  • Humans
  • Immunosuppression Therapy / adverse effects*
  • Immunosuppressive Agents / administration & dosage
  • Immunosuppressive Agents / adverse effects
  • Japan
  • Lymphoma, Large B-Cell, Diffuse / etiology*
  • Lymphoma, Large B-Cell, Diffuse / pathology
  • Lymphoma, Large B-Cell, Diffuse / therapy
  • Male
  • Middle Aged
  • Prednisolone / administration & dosage
  • Radionuclide Imaging
  • Radiotherapy / methods
  • Rituximab
  • Skin Neoplasms / etiology*
  • Skin Neoplasms / pathology
  • Skin Neoplasms / therapy
  • Splenectomy
  • Splenic Neoplasms / etiology*
  • Splenic Neoplasms / pathology
  • Splenic Neoplasms / therapy
  • Tomography, X-Ray Computed
  • Vincristine / administration & dosage

Substances

  • Antibodies, Monoclonal
  • Antibodies, Monoclonal, Murine-Derived
  • Antilymphocyte Serum
  • Immunosuppressive Agents
  • Rituximab
  • Vincristine
  • Doxorubicin
  • Cyclosporine
  • Cyclophosphamide
  • Prednisolone