Regulation of astrocyte inflammatory responses by the Parkinson's disease-associated gene DJ-1

FASEB J. 2009 Aug;23(8):2478-89. doi: 10.1096/fj.08-125153. Epub 2009 Mar 10.

Abstract

The Parkinson's disease (PD)-associated gene DJ-1 mediates direct neuroprotection. The up-regulation of DJ-1 in reactive astrocytes also suggests a role in glia. Here we show that DJ-1 regulates proinflammatory responses in mouse astrocyte-rich primary cultures. When treated with a Toll-like receptor 4 agonist, the bacterial endotoxin lipopolysaccharide (LPS), Dj-1-knockout astrocytes generated >10 times more nitric oxide (NO) than littermate controls. Lentiviral reintroduction of DJ-1 restored the NO response to LPS. The enhanced NO production in Dj-1(-/-) astrocytes was mediated by a signaling pathway involving reactive oxygen species leading to specific hyperinduction of type II NO synthase [inducible NO synthase (iNOS)]. These effects coincided with significantly increased phosphorylation of p38 mitogen-activated protein kinase (MAPK), and p38(MAPK) inhibition suppressed NO production and iNOS mRNA and protein induction. Dj-1(-/-) astrocytes also induced the proinflammatory mediators cyclooxygenase-2 and interleukin-6 significantly more strongly, but not nerve growth factor. Finally, primary neuron cultures grown on Dj-1(-/-) astrocytes became apoptotic in response to LPS in an iNOS-dependent manner, directly demonstrating the neurotoxic potential of astrocytic DJ-1 deficiency. These findings identify DJ-1 as a regulator of proinflammatory responses and suggest that loss of DJ-1 contributes to PD pathogenesis by deregulation of astrocytic neuroinflammatory damage.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Apoptosis / drug effects
  • Astrocytes / drug effects
  • Astrocytes / metabolism*
  • Astrocytes / pathology
  • Base Sequence
  • Cells, Cultured
  • Cyclooxygenase 2 / genetics
  • DNA, Complementary / genetics
  • Enzyme Inhibitors / pharmacology
  • Imidazoles / pharmacology
  • Inflammation / metabolism
  • Inflammation / pathology
  • Intercellular Adhesion Molecule-1 / biosynthesis
  • Interleukin-6 / genetics
  • Lipopolysaccharides / toxicity
  • Mice
  • Mice, Knockout
  • Nitric Oxide / biosynthesis
  • Nitric Oxide Synthase Type II / biosynthesis
  • Oncogene Proteins / deficiency
  • Oncogene Proteins / genetics*
  • Parkinsonian Disorders / genetics*
  • Parkinsonian Disorders / metabolism*
  • Parkinsonian Disorders / pathology
  • Peroxiredoxins
  • Protein Deglycase DJ-1
  • Pyridines / pharmacology
  • Toll-Like Receptor 4 / agonists
  • p38 Mitogen-Activated Protein Kinases / antagonists & inhibitors
  • p38 Mitogen-Activated Protein Kinases / metabolism

Substances

  • DNA, Complementary
  • Enzyme Inhibitors
  • Icam1 protein, mouse
  • Imidazoles
  • Interleukin-6
  • Lipopolysaccharides
  • Oncogene Proteins
  • Pyridines
  • Tlr4 protein, mouse
  • Toll-Like Receptor 4
  • Intercellular Adhesion Molecule-1
  • Nitric Oxide
  • Peroxiredoxins
  • Nitric Oxide Synthase Type II
  • Nos2 protein, mouse
  • Ptgs2 protein, mouse
  • Cyclooxygenase 2
  • p38 Mitogen-Activated Protein Kinases
  • PARK7 protein, mouse
  • Protein Deglycase DJ-1
  • SB 203580