Abstract
The present study reports a case of biopsy-proven pulmonary veno-occlusive disease as a cause of severe pulmonary hypertension in a patient suffering from a chronic myeloproliferative disorder. The pulmonary disease evolved favourably under treatment with defibrotide, a pro-fibrinolytic medication used in hepatic veno-occlusive disease.
MeSH terms
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Aged
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Female
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Fibrinolytic Agents / therapeutic use
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Humans
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Myeloproliferative Disorders / complications*
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Myeloproliferative Disorders / pathology
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Polydeoxyribonucleotides / therapeutic use
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Pulmonary Veno-Occlusive Disease / diagnosis*
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Pulmonary Veno-Occlusive Disease / drug therapy
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Pulmonary Veno-Occlusive Disease / etiology*
Substances
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Fibrinolytic Agents
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Polydeoxyribonucleotides
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defibrotide