Down-regulation of the TGF-beta target gene, PTPRK, by the Epstein-Barr virus encoded EBNA1 contributes to the growth and survival of Hodgkin lymphoma cells

Blood. 2008 Jan 1;111(1):292-301. doi: 10.1182/blood-2006-11-059881. Epub 2007 Aug 24.

Abstract

The Epstein-Barr virus (EBV) contributes to the growth and survival of Hodgkin lymphoma (HL) cells. Here we report that down-regulation of the transforming growth factor-beta (TGF-beta) target gene, protein tyrosine phosphatase receptor kappa (PTPRK), followed EBV infection of HL cells and was also more frequently observed in the Hodgkin and Reed-Sternberg (HRS) cells of EBV-positive compared with EBV-negative primary HL. The viability and proliferation of EBV-positive HL cells was decreased by overexpression of PTPRK, but increased following the knockdown of PTPRK expression in EBV-negative HL cells, demonstrating that PTPRK is a functional tumor suppressor in HL. EBV suppressed the TGF-beta-mediated activation of PTPRK expression, suggesting disruption of TGF-beta signaling upstream of PTPRK. This was confirmed when we showed that the Epstein-Barr nuclear antigen-1 (EBNA1) decreased Smad2 protein levels and that this was responsible for PTPRK down-regulation. EBNA1 decreased the half-life of Smad2 but did not interact with Smad2. By down-regulating Smad2 protein expression, EBNA1 apparently disables TGF-beta signaling, which subsequently decreases transcription of the PTPRK tumor suppressor. We speculate that loss of the phosphatase function of PTPRK may activate as-yet-unidentified growth-promoting protein tyrosine kinases, which in turn contribute to the pathogenesis of EBV-positive HL.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Cell Division / physiology
  • Cell Line
  • Cell Survival / physiology
  • Down-Regulation / physiology
  • Epstein-Barr Virus Infections / complications*
  • Epstein-Barr Virus Nuclear Antigens / metabolism*
  • Female
  • Gene Expression Regulation, Neoplastic
  • Gene Expression Regulation, Viral
  • Genes, Tumor Suppressor / physiology
  • Herpesvirus 4, Human / metabolism*
  • Hodgkin Disease / metabolism
  • Hodgkin Disease / pathology*
  • Hodgkin Disease / virology*
  • Humans
  • Male
  • Receptor-Like Protein Tyrosine Phosphatases, Class 2 / genetics
  • Receptor-Like Protein Tyrosine Phosphatases, Class 2 / metabolism*
  • Smad2 Protein / metabolism
  • Transforming Growth Factor beta / metabolism*

Substances

  • Epstein-Barr Virus Nuclear Antigens
  • SMAD2 protein, human
  • Smad2 Protein
  • Transforming Growth Factor beta
  • PTPRK protein, human
  • Receptor-Like Protein Tyrosine Phosphatases, Class 2
  • EBV-encoded nuclear antigen 1