Assembly of recently translated full-length and C-terminal truncated human gamma-globin chains with a pool of alpha-globin chains to form Hb F in a cell-free system

Arch Biochem Biophys. 2007 Jul 1;463(1):60-7. doi: 10.1016/j.abb.2007.02.030. Epub 2007 Mar 16.

Abstract

Assembly of alpha-globin with translated, full-length and C-terminal truncated human gamma-globin to form Hb F was assessed in a cell-free transcription/translation system. Polysome profiles showed two amino acid C-terminal-truncated gamma-chains retained on polysomes can assemble with unlabeled holo alpha-chains only after puromycin-induced chain release. Two amino acid C-terminal truncated gamma-chains encoded from vectors containing a stop codon at the translation termination site were released from polysomes and assembled with alpha-chains in the absence of puromycin addition, while removal of 11 or more amino acids from the gamma-chain carboxy-terminus inhibited assembly with alpha-chains. These results suggest that amino acids in the HC- and H-helix gamma-chain regions including amino acids 135-144 at the C-terminus in the translated gamma-chains play a key role in assembly with alpha-chains, and that assembly occurs soon after exit of translated gamma-chains from the ribosome tunnel and release from polysomes thereby preventing stable gamma(2) homo-dimer formation.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Blood Proteins / physiology
  • Cell-Free System
  • Fetal Hemoglobin / biosynthesis*
  • Globins / metabolism*
  • Humans
  • Molecular Chaperones / physiology
  • Polyribosomes / metabolism
  • Triticum / metabolism

Substances

  • AHSP protein, human
  • Blood Proteins
  • Molecular Chaperones
  • Globins
  • Fetal Hemoglobin