Adeno-associated virus LPL(S447X) gene therapy in LDL receptor knockout mice

Atherosclerosis. 2007 Sep;194(1):55-61. doi: 10.1016/j.atherosclerosis.2006.09.023. Epub 2006 Nov 7.

Abstract

Background: Overexpression of lipoprotein lipase (LPL) protects against atherosclerosis in genetically engineered mice. We tested whether a gene therapy vector that delivers human (h) LPL(S447X) cDNA to skeletal muscle could induce similar effects.

Methods: LDL receptor knockout (LDLr-/-) mice were injected intramuscular (i.m.) with adeno-associated virus serotype 1 (AAV1) LPL(S447X) or PBS. Four weeks later they were started on an atherogenic diet for 12 weeks. After termination, atherosclerosis was assessed and homogenates of muscle and liver tissue were analyzed.

Results: AAV1-treated mice showed hLPL concentrations of 768+/-293 ng/mL in post-heparin plasma associated with 48% reductions of fasting triglycerides (TG) levels (p<0.0001). In the absence of an effect on total cholesterol (TC) levels, no effects on atherosclerosis were found. An increase in lipid content of injected muscles was accompanied by a significant decrease of TG (-20%, p<0.0001) and free cholesterol (FC) content (-24%, p<0.0001) in liver homogenates.

Conclusions: The data show that transgenic hLPL(S447X) on top of endogenous murine LPL reduces fasting TG levels in plasma but has no effect on atherosclerosis in LDLr-/- mice. While lipid accumulation in the injected muscle was anticipated, this coincided with an interesting decrease of both TG and FC in liver homogenates.

MeSH terms

  • Animals
  • Atherosclerosis / genetics
  • Atherosclerosis / therapy*
  • Cholesterol / blood
  • Dependovirus / genetics*
  • Dietary Fats / pharmacology
  • Fat Emulsions, Intravenous / pharmacology
  • Female
  • Genetic Therapy / methods*
  • Genetic Vectors / genetics
  • Humans
  • Injections, Intramuscular
  • Lipoprotein Lipase / genetics*
  • Lipoprotein Lipase / metabolism
  • Liver / metabolism
  • Mice
  • Mice, Knockout
  • Muscle, Skeletal / physiology
  • Receptors, LDL / genetics*
  • Triglycerides / blood

Substances

  • Dietary Fats
  • Fat Emulsions, Intravenous
  • Receptors, LDL
  • Triglycerides
  • Cholesterol
  • Lipoprotein Lipase