Pathologic consequences of STAT3 hyperactivation by IL-6 and IL-11 during hematopoiesis and lymphopoiesis

Blood. 2007 Mar 15;109(6):2380-8. doi: 10.1182/blood-2006-08-040352. Epub 2006 Nov 2.

Abstract

We have previously demonstrated that STAT3 hyperactivation via the interleukin 6 (IL-6) cytokine family receptor gp130 in gp130 (Y757F/Y757F) mice leads to numerous hematopoietic and lymphoid pathologies, including neutrophilia, thrombocytosis, splenomegaly, and lymphadenopathy. Because IL-6 and IL-11 both signal via a gp130 homodimer, we report here a genetic approach to dissect their individual roles in these pathologies. Neutrophilia and thrombocytosis were absent in gp130 (Y757F/Y757F) mice lacking either IL-6 (gp130 (Y757F/Y757F): IL-6 (-/-)) or the IL-11 receptor alpha subunit (gp130 (Y757F/Y757F): IL-11Ralpha1 (-/-)), and this was associated with a normalized bone marrow compartment. The elevated myelopoiesis and megakaryopoiesis in bone marrow of gp130 (Y757F/Y757F) mice was attributable to an increase by either IL-6 or IL-11 in the STAT3-driven impairment of transforming growth factor beta (TGF-beta) signaling, which is a suppressor of these lineages. In contrast, the absence of IL-6, but not IL-11 signaling, prevented the splenomegaly, abnormal lymphopoiesis, and STAT3 hyperactivation in lymphoid organs of gp130 (Y757F/Y757F) mice. Furthermore, hyperactivation of STAT3 in lymphoid organs was associated with increased expression of IL-6Ralpha, and IL-6Ralpha expression was reduced in gp130 (Y757F/Y757F): Stat3 (+/-) mice displaying normal levels of STAT3 activity. Collectively, these data genetically define distinct roles of IL-6 and IL-11 in driving pathologic hematopoietic and lymphoid responses mediated by STAT3 hyperactivation.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Alleles
  • Animals
  • Cytokine Receptor gp130 / genetics
  • Cytokine Receptor gp130 / metabolism
  • Gene Expression Regulation
  • Hematopoiesis*
  • Interleukin-11 / metabolism*
  • Interleukin-11 / pharmacology
  • Interleukin-6 / deficiency
  • Interleukin-6 / genetics
  • Interleukin-6 / metabolism*
  • Lymphatic Diseases / genetics
  • Lymphatic Diseases / metabolism
  • Lymphatic Diseases / pathology
  • Lymphocytes / cytology*
  • Lymphocytes / metabolism*
  • Mice
  • Mice, Transgenic
  • Receptors, Interleukin-11 / metabolism
  • STAT3 Transcription Factor / metabolism*
  • Signal Transduction
  • Splenomegaly / genetics
  • Splenomegaly / metabolism
  • Splenomegaly / pathology
  • Thrombocytosis / genetics
  • Thrombocytosis / metabolism
  • Thrombocytosis / pathology
  • Transforming Growth Factor beta1 / metabolism

Substances

  • Il6st protein, mouse
  • Interleukin-11
  • Interleukin-6
  • Receptors, Interleukin-11
  • STAT3 Transcription Factor
  • Transforming Growth Factor beta1
  • Cytokine Receptor gp130