The Rx-like homeobox gene (Rx-L) is necessary for normal photoreceptor development

Invest Ophthalmol Vis Sci. 2006 Oct;47(10):4245-53. doi: 10.1167/iovs.06-0167.

Abstract

Purpose: The retinal homeobox (Rx) gene plays an essential role in retinal development. An Rx-like (Rx-L) gene from Xenopus laevis has been identified. The purpose of this study was to analyze the function of Rx-L in the developing retina.

Methods: DNA-binding properties of Rx-L were analyzed by electrophoretic mobility shift assay (EMSA), with in vitro-translated proteins and radiolabeled oligonucleotide probe. The Rx-L expression pattern was analyzed by in situ hybridization using whole or sectioned embryos and digoxigenin-labeled antisense riboprobes. Rx-L loss of function was studied by using antisense morpholino oligonucleotides targeted to the Rx-L translation initiation site. Embryos injected with control or Rx-L morpholinos were analyzed at stage 41 or 45.

Results: Rx-L shares homology with Rx at the homeo-, OAR, and Rx domains, but lacks an octapeptide motif. Rx-L is expressed in the developing retina beginning in the early tailbud stage. In the maturing retina, Rx-L expression is restricted primarily to the developing photoreceptor layer and the ciliary marginal zone. Rx-L can bind a photoreceptor conserved element-1 (PCE-1) oligonucleotide, an element conserved among all known photoreceptor gene promoters. In a promoter activity assay, Rx-L functions as a stronger transcriptional activator than Rx. Antisense morpholino-mediated knockdown of Rx-L expression resulted in a decrease in rhodopsin and red cone opsin expression levels in Xenopus retinas. Injection of the Rx-L antisense morpholino oligonucleotide also resulted in a decrease in the length of both rod and cone outer segments.

Conclusions: The results suggest that Rx-L functions to regulate rod and cone development by activating photoreceptor-specific gene expression.

Publication types

  • Research Support, N.I.H., Extramural

MeSH terms

  • Amino Acid Sequence
  • Animals
  • Electrophoretic Mobility Shift Assay
  • Eye Proteins / genetics*
  • Gene Expression Regulation, Developmental / physiology*
  • Homeodomain Proteins / genetics*
  • Immunohistochemistry
  • In Situ Hybridization
  • Molecular Sequence Data
  • Oligonucleotide Probes / chemistry
  • Photoreceptor Cells, Vertebrate / cytology
  • Photoreceptor Cells, Vertebrate / physiology*
  • Retina / embryology*
  • Reverse Transcriptase Polymerase Chain Reaction
  • Sequence Homology, Amino Acid
  • Transcription Factors / genetics*
  • Xenopus laevis

Substances

  • Eye Proteins
  • Homeodomain Proteins
  • Oligonucleotide Probes
  • Transcription Factors