Metabolism of branched chain fatty acids in peroxisomal disorders

J Inherit Metab Dis. 1990;13(3):387-9. doi: 10.1007/BF01799402.
No abstract available

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adrenoleukodystrophy / metabolism
  • Cells, Cultured
  • Chondrodysplasia Punctata / metabolism
  • Fatty Acids / metabolism*
  • Fibroblasts / ultrastructure
  • Heptanoic Acids / metabolism
  • Humans
  • Metabolism, Inborn Errors / metabolism*
  • Microbodies / metabolism*
  • Oxidation-Reduction
  • Refsum Disease / metabolism
  • Stearic Acids / metabolism
  • Zellweger Syndrome / metabolism

Substances

  • Fatty Acids
  • Heptanoic Acids
  • Stearic Acids
  • 4,8,12,16-tetramethylheptanoic acid
  • stearic acid
  • pristanic acid