[Beta-Thalassemia in Poland. I. Mediterranean mutations in beta-thalassemia]

Pol Merkur Lekarski. 2006 Jan;20(115):53-6.
[Article in Polish]

Abstract

The aim of the present investigation was to verify a common view that thalassemia in Poland is a very rare disease.

Material and methods: 600 patients (270 male and 330 female) aged 2-85 years with microcytosis and no evidence of iron deficiency were examined for beta-thalassemia. Hemoglobin A2 and hemoglobin F and bilirubin were evaluated. Patients with elevated A2 hemoglobin concentration were examined for 8 common Mediterranean mutations.

Results: Hemoglobin A2 was increased in 106 patients. In 48 patients there was also an elevation of hemoglobin F and in 42 - of serum bilirubin. 7 different mutations were detected in 46 heterozygous patients (numbers of patients with a particular mutation are in square brackPis): IVS1-6(T>C) [15], IVS2-745(C>G) [14], IVS2-1(G>A) [10], IVS1-1(G>A) [2], CD6-A [2], CD39(C>T) [2], IVS1-110(G>A) [1].

Conclusions: Frequencies of individual mutations in Poland were different from those encountered in Mediterranean and some Central European countries. Our data indicate that fl-thalassemia in Poland is not a rare disease and should be considered in differential diagnosis of hypochromic anemia.

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • Aged, 80 and over
  • Bilirubin / blood
  • Catchment Area, Health
  • Child
  • Child, Preschool
  • Female
  • Fetal Hemoglobin / metabolism
  • Humans
  • Male
  • Mediterranean Region
  • Middle Aged
  • Point Mutation / genetics*
  • Poland / epidemiology
  • beta-Thalassemia / blood
  • beta-Thalassemia / epidemiology*
  • beta-Thalassemia / genetics*

Substances

  • Fetal Hemoglobin
  • Bilirubin