Abstract
Primary angiosarcoma of the spleen is rare and the prognosis is very poor. The authors present a 2-year-old girl with spontaneous rupture of splenic angiosarcoma. At diagnosis there were liver metastases. After splenectomy she received chemotherapy with ifosfamide, vincristine, and actinomycine D combined with a partial liver resection. She remained in complete remission over 2 years from diagnosis.
MeSH terms
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Antineoplastic Combined Chemotherapy Protocols / therapeutic use
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Child, Preschool
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Female
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Hemangiosarcoma / diagnosis
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Hemangiosarcoma / secondary*
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Hemangiosarcoma / therapy
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Hepatectomy
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Humans
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Liver Neoplasms / diagnosis
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Liver Neoplasms / secondary*
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Liver Neoplasms / therapy
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Neoplasm Metastasis
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Prognosis
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Remission Induction
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Splenic Neoplasms / diagnosis
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Splenic Neoplasms / pathology*
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Splenic Neoplasms / therapy