[An autopsy case of intestinal Behcet's disease with sacroiliitis accompanied by myelodysplastic syndrome with trisomy 8]

Rieko Tsubata; Fumihito Suzuki; Takehiko Sugihara; Jun Ogawa; Hiroyuki Hagiyama; Toshihiro Nanki; Hitoshi Kohsaka; Tetsuo Kubota; Nobuyuki Miyasaka

doi:10.2177/jsci.28.48

[An autopsy case of intestinal Behcet's disease with sacroiliitis accompanied by myelodysplastic syndrome with trisomy 8]

Nihon Rinsho Meneki Gakkai Kaishi. 2005 Feb;28(1):48-55. doi: 10.2177/jsci.28.48.

[Article in Japanese]

Authors

Rieko Tsubata¹, Fumihito Suzuki, Takehiko Sugihara, Jun Ogawa, Hiroyuki Hagiyama, Toshihiro Nanki, Hitoshi Kohsaka, Tetsuo Kubota, Nobuyuki Miyasaka

Affiliation

¹ Department of Rheumatology, Tokyo Medical and Dental University, Tokyo, Japan.

PMID: 15744121
DOI: 10.2177/jsci.28.48

Abstract

Here we described an autopsy case of intestinal Behcet's disease with sacroiliitis associated with myelodysplastic syndrome (RAEB-t, 8+). Over twenty cases of Behcet's disease associated with myelodysplastic syndrome have been reported in preliterature so far. The majority of them are incomplete type of Behcet's disease having intestinal ulceration. Of those, trisomy 8 is the most common chromosomal abnormality. We reviewed similar cases reported and investigated the association of intestinal Behcet's disease with trisomy 8. The association of sacroiliitis with Behcet's disease is also studied.

Publication types

Case Reports
English Abstract
Review

MeSH terms

Aged
Anemia, Refractory, with Excess of Blasts / complications*
Anemia, Refractory, with Excess of Blasts / genetics
Behcet Syndrome / complications*
Chromosomes, Human, Pair 8*
Humans
Ileal Diseases / complications*
Male
Sacrum*
Spondylitis / complications*
Trisomy*
Ulcer / complications*