Combined general and epidural anesthesia for a child with alagille syndrome: a case report

Paediatr Anaesth. 2004 Sep;14(9):787-91. doi: 10.1111/j.1460-9592.2004.01285.x.

Abstract

Alagille syndrome (syndromic paucity of interlobular bile ducts) is the most common form of familial intrahepatic cholestasis. We describe the perioperative management of a pediatric patient with Alagille syndrome undergoing ileal exclusion and the specific issues associated with epidural anesthesia with this syndrome.

Publication types

  • Case Reports

MeSH terms

  • Alagille Syndrome / surgery*
  • Anesthesia, Epidural / methods*
  • Anesthesia, General / methods*
  • Anesthetics, Combined / therapeutic use*
  • Anesthetics, Inhalation / therapeutic use
  • Anesthetics, Intravenous / therapeutic use
  • Anesthetics, Local / therapeutic use
  • Atracurium / analogs & derivatives*
  • Atracurium / therapeutic use
  • Bupivacaine / therapeutic use
  • Child, Preschool
  • Colostomy / methods
  • Fentanyl / therapeutic use*
  • Humans
  • Ileum / surgery
  • Intubation, Intratracheal / methods
  • Isoflurane / therapeutic use
  • Male
  • Midazolam / therapeutic use
  • Neuromuscular Blocking Agents / therapeutic use
  • Thiopental / therapeutic use

Substances

  • Anesthetics, Combined
  • Anesthetics, Inhalation
  • Anesthetics, Intravenous
  • Anesthetics, Local
  • Neuromuscular Blocking Agents
  • Atracurium
  • Isoflurane
  • Thiopental
  • cisatracurium
  • Midazolam
  • Fentanyl
  • Bupivacaine