Abstract
Alagille syndrome (syndromic paucity of interlobular bile ducts) is the most common form of familial intrahepatic cholestasis. We describe the perioperative management of a pediatric patient with Alagille syndrome undergoing ileal exclusion and the specific issues associated with epidural anesthesia with this syndrome.
MeSH terms
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Alagille Syndrome / surgery*
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Anesthesia, Epidural / methods*
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Anesthesia, General / methods*
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Anesthetics, Combined / therapeutic use*
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Anesthetics, Inhalation / therapeutic use
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Anesthetics, Intravenous / therapeutic use
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Anesthetics, Local / therapeutic use
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Atracurium / analogs & derivatives*
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Atracurium / therapeutic use
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Bupivacaine / therapeutic use
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Child, Preschool
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Colostomy / methods
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Fentanyl / therapeutic use*
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Humans
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Ileum / surgery
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Intubation, Intratracheal / methods
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Isoflurane / therapeutic use
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Male
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Midazolam / therapeutic use
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Neuromuscular Blocking Agents / therapeutic use
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Thiopental / therapeutic use
Substances
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Anesthetics, Combined
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Anesthetics, Inhalation
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Anesthetics, Intravenous
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Anesthetics, Local
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Neuromuscular Blocking Agents
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Atracurium
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Isoflurane
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Thiopental
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cisatracurium
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Midazolam
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Fentanyl
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Bupivacaine