Initial management of complex pediatric disorders: prunebelly syndrome, posterior urethral valves

Urol Clin North Am. 2004 Aug;31(3):399-415, vii. doi: 10.1016/j.ucl.2004.04.010.

Abstract

Prunebelly syndrome and posterior urethral valves are conditions of detrusor dysfunction associated with antenatal urethral obstruction. The resultant severe hydroureteronephrosis and renal dysplasia initiate a sequence potentially leading to renal failure. This article reviews clinical features and explores neonatal evaluation and treatment for both conditions. A comprehensive approach to initial management aimed at optimal renal preservation and bladder rehabilitation is proposed.

Publication types

  • Review

MeSH terms

  • Cryptorchidism / etiology
  • Humans
  • Hydronephrosis / etiology
  • Hydronephrosis / therapy
  • Infant, Newborn
  • Male
  • Prune Belly Syndrome / diagnosis
  • Prune Belly Syndrome / therapy*
  • Ultrasonography, Prenatal
  • Urethra / abnormalities*
  • Urination Disorders / etiology
  • Urination Disorders / therapy
  • Urodynamics