Background: Double-chambered left ventricle (DCLV) is a rare congenital anomaly, and only a few cases in which a 2-chambered LV is separated by the interventricular septum or an abnormal muscle bundle have been reported in the literature. Frequently, such cases are diagnosed when a patient is admitted to hospital for the evaluation of a cardiac murmur, and most of these patients have isolated DCLV.
Materials and methods: We describe the case of a 13-year-old girl with DCLV who had twice undergone operation, including mitral valve replacement, in our institution.
Result: No gradient was found after surgical resection of the hypertrophic floating mass, and the patient's symptoms disappeared.
Discussion: Surgical resection can be carried out in patients with DCLV when done sufficiently early, and careful echocardiographic examination is important in a continuing follow-up. Surgeons should keep in mind the possibility of a recurrence of DCLV.