[Cerebrotendinous xanthomatosis--a treatable metabolic disorder]

Nervenarzt. 2004 Jun;75(6):608. doi: 10.1007/s00115-003-1500-y.
[Article in German]
No abstract available

Publication types

  • Case Reports
  • Comment
  • Letter

MeSH terms

  • Adult
  • Brain / pathology
  • Chenodeoxycholic Acid / therapeutic use*
  • Cholestanol / blood
  • Cholesterol / blood
  • Chromosome Aberrations
  • Diagnosis, Differential
  • Female
  • Follow-Up Studies
  • Genes, Recessive
  • Humans
  • Magnetic Resonance Imaging
  • Male
  • Middle Aged
  • Neurologic Examination
  • Steroid Hydroxylases / deficiency
  • Treatment Outcome
  • Triglycerides / blood
  • Xanthomatosis, Cerebrotendinous / diagnosis
  • Xanthomatosis, Cerebrotendinous / drug therapy*
  • Xanthomatosis, Cerebrotendinous / genetics
  • Xanthomatosis, Cerebrotendinous / mortality

Substances

  • Triglycerides
  • Chenodeoxycholic Acid
  • Cholestanol
  • Cholesterol
  • Steroid Hydroxylases