von Willebrand factor as a marker of endothelial cell activation following BMT

Bone Marrow Transplant. 1992 Dec;10(6):499-506.

Abstract

Endothelial cell activation may play a role in thrombotic complications of BMT such as hepatic veno-occlusive disease (VOD), right atrial line thrombosis and microangiopathic haemolysis. To assess this, von Willebrand factor antigen (vWF:ag) was measured in 72 patients (25 allografts, 46 autografts and one syngeneic) during the first 6 weeks post-transplant. There was a significant rise in vWF:ag in both allografts and autografts but a greater increase was seen in the allografts. The changes in vWF:ag did not correlate with changes in C reactive protein showing that this was not merely an acute phase response. vWF multimers were normal in a subgroup of uncomplicated transplants showing that there was no large scale endothelial cell disruption. Patients with VOD did not have changes in vWF:ag that were consistently different from uncomplicated controls. Three of four patients who developed line thrombosis had higher levels of vWF:ag compared with control groups; multimeric structure of the vWF was again normal. These results show that there is endothelial cell activation post-BMT and that this is greater in allografts compared with autografts, thus suggesting a possible mechanism for the higher incidence of VOD in this group. There were no useful predictive markers of VOD or thrombosis in individual patients.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Adult
  • Anemia, Hemolytic / etiology
  • Biomarkers / blood
  • Bone Marrow Transplantation / adverse effects*
  • Child
  • Child, Preschool
  • Endothelium, Vascular / metabolism*
  • Female
  • Hepatic Veno-Occlusive Disease / etiology
  • Humans
  • Male
  • Middle Aged
  • Thrombosis / etiology
  • Time Factors
  • von Willebrand Factor / metabolism*

Substances

  • Biomarkers
  • von Willebrand Factor