Rhabdomyosarcomas are potential target of MAGE-specific immunotherapies

Cancer Immunol Immunother. 2004 Jun;53(6):519-24. doi: 10.1007/s00262-003-0484-6. Epub 2004 Jan 16.

Abstract

The search for alternative strategies of therapy remains a major issue for most neoplastic diseases. The expression of several tumor antigens makes human rhabdomyosarcomas, which are the most frequent form of soft tissue tumor in children, a good candidate for tumor-specific immunotherapy. To assess the feasibility of this approach, we evaluated the ability of rhabdomyosarcoma cell lines to process and present the MAGE-A tumor antigens to effectors of the immune system. To this end, we investigated recognition of MAGE-A-positive rhabdomyosarcoma cells by HLA-B*3701-restricted T cells specific for a MAGE-A-derived peptide. Low level of HLA expression impaired recognition of the tumor cells. Therefore, to obtain HLA expression avoiding the use of IFN-gamma and TNF-alpha, which could affect the proteasome activity, a rhabdomyosarcoma line was transduced by a retroviral vector encoding the HLA-B*3701 allele. Recognition of the infected cells was then observed also in the absence of IFN-gamma and TNF-alpha treatment, thus demonstrating that rhabdomyosarcoma cells were indeed able to naturally process and present the MAGE-A antigens. These results demonstrate that rhabdomyosarcoma cells expressing MAGE-A can be targets of tumor-specific effectors, suggesting the feasibility of clinical protocols of specific immunotherapy also for the treatment of rhabdomyosarcoma.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Antigens, Neoplasm / genetics
  • Antigens, Neoplasm / immunology*
  • B-Lymphocytes / immunology
  • B-Lymphocytes / pathology
  • Feasibility Studies
  • HLA-B Antigens / genetics
  • HLA-B Antigens / pharmacology
  • Humans
  • Immunotherapy*
  • Interferon-gamma / immunology
  • Melanoma / immunology
  • Melanoma / pathology
  • Melanoma-Specific Antigens
  • Neoplasm Proteins / genetics
  • Neoplasm Proteins / immunology*
  • Reverse Transcriptase Polymerase Chain Reaction
  • Rhabdomyosarcoma / immunology*
  • Rhabdomyosarcoma / pathology
  • Skin Neoplasms / immunology
  • Skin Neoplasms / pathology
  • T-Lymphocytes / immunology*
  • T-Lymphocytes, Cytotoxic / immunology
  • Tumor Cells, Cultured
  • Tumor Necrosis Factor-alpha / immunology
  • Tumor Necrosis Factor-alpha / metabolism

Substances

  • Antigens, Neoplasm
  • HLA-B Antigens
  • MAGEA3 protein, human
  • Mage-a2 antigen
  • Melanoma-Specific Antigens
  • Neoplasm Proteins
  • Tumor Necrosis Factor-alpha
  • Interferon-gamma