Severe unilateral pulmonary vascular changes in child with polysplenia

Asian Cardiovasc Thorac Ann. 2002 Dec;10(4):359-61. doi: 10.1177/021849230201000422.

Abstract

A 12-year-old boy with polysplenia and single ventricle experienced recurrent episodes of pneumonia, hemoptysis, and pulmonary hypertension. Unilateral pulmonary vein obstruction was diagnosed, and a left pneumonectomy was performed. Microscopy of the resected specimen revealed pulmonary veno-occlusive disease in the small pulmonary venules, and old arteritis in the small pulmonary arteries.

Publication types

  • Case Reports

MeSH terms

  • Arteritis / complications*
  • Arteritis / pathology*
  • Arteritis / surgery
  • Child
  • Hemoptysis / etiology*
  • Hemoptysis / pathology*
  • Hemoptysis / surgery
  • Humans
  • Hypertension, Pulmonary / etiology*
  • Hypertension, Pulmonary / pathology*
  • Hypertension, Pulmonary / surgery
  • Male
  • Pneumonectomy
  • Pneumonia / etiology*
  • Pneumonia / pathology*
  • Pneumonia / surgery
  • Pulmonary Artery / pathology*
  • Pulmonary Artery / surgery
  • Pulmonary Circulation
  • Pulmonary Veno-Occlusive Disease / complications*
  • Pulmonary Veno-Occlusive Disease / pathology*
  • Pulmonary Veno-Occlusive Disease / surgery
  • Severity of Illness Index
  • Splenic Diseases / complications*
  • Splenic Diseases / pathology*
  • Splenic Diseases / surgery