C1 fixation and classical complement pathway activation by a fragment of the Cmu4 domain of IgM

J Exp Med. 1975 Nov 1;142(5):1322-6. doi: 10.1084/jem.142.5.1322.

Abstract

A 56 residue fragment derived from a Waldenströme IgM protein and consisting of 24 residues of the amino-terminal portion of the Cmu4 domain disulfide bonded to 32 residues of the carboxy-terminal region of the loop has been shown to fix active C1 (C1) in a C1-fixation assay. Cleavage of the disulfide bond within the CH4 fragment resulted in a marked decrease of C1-fixing ability, although the isolated A and B fragments did retain a limited ability to fix C1. Upon incubation with normal human serum the intact CH4 fragment and equal molar amounts of the isolated A and B peptides consumed C4 suggesting that the C1-activating determinant of IgM remains intact in these three fragments. Furthermore, on a molar basis the intact or the reduced CH4 fragment consumed C4 as effectively as each of its component chains suggesting that transient binding of C1 by the individual A and B peptide chains is sufficient to activate C1. On the basis of these observations it is proposed that a classical complement fixation function, i.e. C1 binding and activation, can be localized within a region of the IgM molecule corresponding to the Cmu4 domain.

Publication types

  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Amino Acid Sequence
  • Complement C1 / metabolism*
  • Complement Fixation Tests
  • Complement System Proteins / metabolism*
  • Humans
  • Immunoglobulin Fragments*
  • Immunoglobulin M* / metabolism
  • Molecular Weight

Substances

  • Complement C1
  • Immunoglobulin Fragments
  • Immunoglobulin M
  • Complement System Proteins