Structural requirements of anticoagulant protein S for its binding to the complement regulator C4b-binding protein

J Biol Chem. 2002 Apr 26;277(17):15099-106. doi: 10.1074/jbc.M103036200. Epub 2002 Feb 14.

Abstract

The vitamin K-dependent anticoagulant protein S binds with high affinity to C4b-binding protein (C4BP), a regulator of complement. Despite the physiological importance of the complex, we have only a patchy view of the C4BP-binding site in protein S. Based on phage display experiments, protein S residues 447-460 were suggested to form part of the binding site. Several experimental approaches were now used to further elucidate the structural requirements for protein S binding to C4BP. Peptides comprising residues 447-460, 451-460, or 453-460 of protein S were found to inhibit the protein S-C4BP interaction, whereas deletion of residues 459-460 from the peptide caused complete loss of inhibition. In recombinant protein S, each of residues 447-460 was mutated to Ala, and the protein S variants were tested for binding to C4BP. The Y456A mutation reduced binding to C4BP approximately 10-fold, and a peptide corresponding to residues 447-460 of this mutant was less inhibitory than the parent peptide. A further decrease in binding was observed using a recombinant variant in which a site for N-linked glycosylation was moved from position 458 to 456 (Y456N/N458T). A monoclonal antibody (HPSf) selective for free protein S reacted poorly with the Y456A variant but reacted efficiently with the other variants. A second antibody, HPS 34, which partially inhibited the protein S-C4BP interaction, reacted poorly with several of the Ala mutants, suggesting that its epitope was located in the 451-460 region. Phage display analysis of the HPS 34 antibody further identified this region as its epitope. Taken together, our results suggest that residues 453-460 of protein S form part of a more complex binding site for C4BP. A recently developed three-dimensional model of the sex hormone-binding globulin-like region of protein S was used to analyze available experimental data.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Amino Acid Sequence
  • Anticoagulants / chemistry
  • Anticoagulants / metabolism*
  • Complement C4b / metabolism*
  • Complement Inactivator Proteins*
  • Epitope Mapping
  • Glycoproteins*
  • Glycosylation
  • Humans
  • Models, Molecular
  • Molecular Sequence Data
  • Mutagenesis, Site-Directed
  • Protein Binding
  • Protein Conformation
  • Protein S / chemistry
  • Protein S / genetics
  • Protein S / metabolism*
  • Receptors, Complement / metabolism*
  • Recombinant Proteins / chemistry
  • Recombinant Proteins / genetics
  • Recombinant Proteins / metabolism
  • Sex Hormone-Binding Globulin / metabolism
  • Surface Plasmon Resonance

Substances

  • Anticoagulants
  • Complement Inactivator Proteins
  • Glycoproteins
  • Protein S
  • Receptors, Complement
  • Recombinant Proteins
  • Sex Hormone-Binding Globulin
  • Complement C4b