We report the case of a 15-year-old boy with primary high grade angiosarcoma of the 6th rib. The patient underwent chest wall resection (3 ribs) and reconstruction by using a sandwich of Marlex mesh with strips of methyl methacrylate. No adjuvant treatment was administered. A favourable outcome was observed, with no recurrence at 6-year follow-up. Functional results were excellent as well, with complete return of the patient to normal activities.