Chylothorax complicating Gorham's disease

Ann Thorac Surg. 2001 Sep;72(3):937-9. doi: 10.1016/s0003-4975(00)02417-6.

Abstract

Gorham's disease is a rare disorder characterized by a proliferation of thin-walled lymphatic vessels (lymphangiectasia) resulting in an osteolysis. A chylothorax is present in about one-fifth of the patients and carries a poor prognosis. In this circumstance, surgery including thoracic duct ligation, pleurodesis, and excision of involved tissue is probably the treatment of choice. It is facilitated by a precise radiological assessment using a computed tomographic scanning coupled with a lymphography. We report such a case.

Publication types

  • Case Reports

MeSH terms

  • Chylothorax / complications*
  • Chylothorax / diagnostic imaging
  • Chylothorax / surgery
  • Female
  • Humans
  • Middle Aged
  • Osteolysis, Essential / complications*
  • Radiography, Thoracic
  • Tomography, X-Ray Computed