Glial cell death induced by overexpression of alpha-synuclein

J Neurosci Res. 2001 Sep 1;65(5):432-8. doi: 10.1002/jnr.1171.

Abstract

alpha-Synuclein is present in intracellular protein aggregates that are hallmarks of common neurodegenerative disorders including Parkinson disease, dementia with Lewy bodies, and multiple system atrophy. alpha-Synuclein is localized in neurons and presynaptic terminals. Under pathological conditions, however, it is also found in glia. The role of alpha-synuclein in glial cells and its relevance to the molecular pathology of neurodegenerative diseases is presently unclear. To investigate the consequence of alpha-synuclein overexpression in glia, we transfected U373 astrocytoma cells with vectors encoding wild-type human alpha-synuclein or C-terminally truncated synuclein fused to red fluorescent protein. alpha-synuclein immunocytochemistry of transfected astroglial cells revealed diffuse cytoplasmic labeling associated with discrete inclusions both within cell bodies and processes. Susceptibility to oxidative stress was increased in astroglial cells overexpressing alpha-synuclein, particularly in the presence of cytoplasmic inclusions. Furthermore, overexpression of alpha-synuclein induced apoptotic death of astroglial cells as shown by TUNEL staining. Our in vitro model is the first to replicate salient features of the glial pathology associated with alpha-synucleinopathies. It provides a simple testbed to further explore the cascade of events that leads to apoptotic glial cell death in some of these disorders; it may also be useful to assess the effects of therapeutic interventions including antioxidative and antiapoptotic strategies.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Apoptosis / genetics*
  • Astrocytes / metabolism*
  • Astrocytes / pathology
  • Cell Size / genetics
  • Green Fluorescent Proteins
  • Humans
  • Immunohistochemistry
  • Indicators and Reagents / pharmacokinetics
  • L-Lactate Dehydrogenase / analysis
  • Luminescent Proteins / pharmacokinetics
  • Nerve Degeneration / genetics
  • Nerve Degeneration / metabolism*
  • Nerve Degeneration / pathology
  • Nerve Tissue Proteins / genetics*
  • Nerve Tissue Proteins / metabolism
  • Neurodegenerative Diseases / genetics
  • Neurodegenerative Diseases / metabolism*
  • Neurodegenerative Diseases / pathology
  • Oxidative Stress / physiology*
  • Peptide Fragments / genetics
  • Protein Structure, Tertiary / genetics
  • Recombinant Fusion Proteins / genetics
  • Red Fluorescent Protein
  • Synucleins
  • Transfection
  • Tumor Cells, Cultured
  • alpha-Synuclein

Substances

  • Indicators and Reagents
  • Luminescent Proteins
  • Nerve Tissue Proteins
  • Peptide Fragments
  • Recombinant Fusion Proteins
  • SNCA protein, human
  • Synucleins
  • alpha-Synuclein
  • Green Fluorescent Proteins
  • L-Lactate Dehydrogenase