Beckwith-Wiedemann syndrome and virilizing cortical adrenal tumor in a child

J Pediatr Surg. 2000 Aug;35(8):1269-71. doi: 10.1053/jpsu.2000.8771.

Abstract

The authors report a case of a virilizing adrenal tumor that developed in a 2-year-old child with Beckwith-Wiedemann syndrome (BWS). He had a fetal diagnosis of omphalocele and a history of neonatal adrenal cysts. The importance of prenatal diagnosis of BWS and postnatal follow-up of tumors is discussed. The differential diagnosis of adrenal pathologies occurring in BWS also is reviewed.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Adrenal Cortex Neoplasms / complications*
  • Adrenal Cortex Neoplasms / diagnosis
  • Beckwith-Wiedemann Syndrome / complications*
  • Beckwith-Wiedemann Syndrome / diagnosis
  • Child, Preschool
  • Follow-Up Studies
  • Humans
  • Male
  • Prenatal Diagnosis
  • Time Factors
  • Virilism / etiology