Prion diseases: a typical Kuhnian abnormality in a molecular paradigm

Med Hypotheses. 2000 Jan;54(1):69-71. doi: 10.1054/mehy.1998.0837.

Abstract

As a new class of pathogens with unusual properties, prions have been implied in several spongiform encephalopathies mainly affecting farm animals (scrapie, mad-cow disease) and humans (kuru, Creutzfeldt-Jacob disease, fatal familial insomnia) (1). The term prions underlines the feature that the agents would merely consist of a protein (2), perhaps a pathological counterpart of a cellular constituent with poorly defined functions (3-5). In reviewing relevant literature, in order to test the validity of the 'protein-only hypothesis' for coherence and consistency with a molecular paradigm, we have met evident discrepancies, making prion diseases a typical abnormality in a Kuhnian sense. This paper summarizes and analyses the main features of the protein-only model.

MeSH terms

  • Animals
  • Models, Biological
  • Phylogeny
  • Prion Diseases / genetics*
  • Prions / genetics

Substances

  • Prions