Structural basis for the anticoagulant activity of the thrombin-thrombomodulin complex

Nature. 2000 Mar 30;404(6777):518-25. doi: 10.1038/35006683.

Abstract

The serine proteinase alpha-thrombin causes blood clotting through proteolytic cleavage of fibrinogen and protease-activated receptors and amplifies its own generation by activating the essential clotting factors V and VIII. Thrombomodulin, a transmembrane thrombin receptor with six contiguous epidermal growth factor-like domains (TME1-6), profoundly alters the substrate specificity of thrombin from pro- to anticoagulant by activating protein C. Activated protein C then deactivates the coagulation cascade by degrading activated factors V and VIII. The thrombin-thrombomodulin complex inhibits fibrinolysis by activating the procarboxypeptidase thrombin-activatable fibrinolysis inhibitor. Here we present the 2.3 A crystal structure of human alpha-thrombin bound to the smallest thrombomodulin fragment required for full protein-C co-factor activity, TME456. The Y-shaped thrombomodulin fragment binds to thrombin's anion-binding exosite-I, preventing binding of procoagulant substrates. Thrombomodulin binding does not seem to induce marked allosteric structural rearrangements at the thrombin active site. Rather, docking of a protein C model to thrombin-TME456 indicates that TME45 may bind substrates in such a manner that their zymogen-activation cleavage sites are presented optimally to the unaltered thrombin active site.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Amino Acid Sequence
  • Anticoagulants / chemistry*
  • Carboxypeptidase B2
  • Carboxypeptidases / chemistry
  • Crystallography, X-Ray
  • Humans
  • Macromolecular Substances
  • Models, Molecular
  • Molecular Sequence Data
  • Peptide Fragments / chemistry
  • Protein Binding
  • Protein C / chemistry
  • Protein Conformation
  • Protein Structure, Tertiary
  • Static Electricity
  • Structure-Activity Relationship
  • Thrombin / chemistry*
  • Thrombin / physiology
  • Thrombomodulin / chemistry*
  • Thrombomodulin / physiology

Substances

  • Anticoagulants
  • Macromolecular Substances
  • Peptide Fragments
  • Protein C
  • Thrombomodulin
  • Carboxypeptidases
  • Carboxypeptidase B2
  • Thrombin

Associated data

  • PDB/1AOH
  • PDB/1DX5
  • PDB/1PFX