Human glycosylation disorders and sugar supplement therapy

Biochem Biophys Res Commun. 1999 Feb 16;255(2):189-93. doi: 10.1006/bbrc.1998.9945.

Abstract

Some genetic defects in protein glycosylation can be treated effectively with dietary supplements of monosaccharides. An easy screening test and non-toxic therapy for potentially lethal disorders should encourage physicians to search for more patients with glycosylation disorders. It should also stimulate research on the occurrence and availability of monosaccharides used for glycoconjugate synthesis and for vertebrate models to study their utilization.

Publication types

  • Research Support, U.S. Gov't, P.H.S.
  • Review

MeSH terms

  • Carbohydrate Metabolism, Inborn Errors / diet therapy*
  • Carbohydrate Metabolism, Inborn Errors / genetics
  • Carbohydrate Metabolism, Inborn Errors / metabolism*
  • Dietary Carbohydrates / therapeutic use*
  • Glycosylation
  • Humans
  • Monosaccharides / therapeutic use*

Substances

  • Dietary Carbohydrates
  • Monosaccharides